What is RV dependent coronary circulation?

RVDCC was defined as the presence of any coronary-cameral fistula with coronary obstruction proximal to the fistula and angiographic evidence of RV perfusion of the myocardium through the fistulous communication.

What are coronary Sinusoids?

Severe right ventricle hypoplasia can result in fistulous connections from the right ventricle and to the coronary artery, called coronary sinusoids, which might be essential for coronary circulation. Pulmonary atresia with VSD is considered a severe type of Tetralogy of Fallot.

What is PA IVS?

DEFINITION. PA/IVS is a rare congenital cardiac defect that consists of atresia of the pulmonary valve resulting in an absent connection between the right ventricular outflow tract (RVOT) and pulmonary arteries as well as an IVS that allows no connection between the right and left ventricles.

What does intact ventricular septum mean?

The ventricular septum is the wall between the two pumping chambers of the heart. In pulmonary atresia with intact ventricular septum, this wall is intact. Babies born with pulmonary atresia don’t have enough oxygen in their blood to support the body’s needs. Treatment at birth is necessary for survival.

What drains into coronary sinus?

The coronary sinus receives drainage from most epicardial ventricular veins, including the oblique vein of the left atrium (and other left and right atrial veins), the great cardiac vein, the posterior vein of the left ventricle, the left marginal vein, and the posterior interventricular vein.

Which cardiac vein travels with the left marginal artery?

Left marginal artery
Vein left marginal vein
Supplies left ventricle
Identifiers
Latin ramus marginalis sinister arteriae coronariae sinistrae

Does the coronary sinus bring blood to the heart?

The function of the coronary sinus is to receive deoxygenated blood from the epicardial ventricular veins, which are the veins of the heart muscle. The coronary sinus delivers this blood to the right atrium before it eventually travels back to the lungs to be oxygenated again.

How do you get to the coronary sinus?

The coronary sinus drains into the right atrium, at the coronary sinus orifice, an opening between the inferior vena cava and the right atrioventricular orifice or tricuspid valve….

Coronary sinus
Precursor Sinus venosus
Source Great cardiac vein
Drains to Right atrium
Identifiers

What is IVS on Echo?

IVS=Interventricular septum, LVID=left ventricle inner dimension, LVPW=left ventricle posterior wall. Figure 1. Echocardiographic measurement.

What is the survival rate of pulmonary atresia?

Pulmonary atresia with VSD is the ultimate form of tetralogy of Fallot and is estimated to represent 5% to 10% of tetralogy of Fallot patients. The survival rate without surgical repair is as low as 50% at 1 year of age and 8% at 10 years.

What is hypoplastic left heart syndrome?

Hypoplastic left heart syndrome (HLHS) is a birth defect that affects normal blood flow through the heart. As the baby develops during pregnancy, the left side of the heart does not form correctly. Hypoplastic left heart syndrome is one type of congenital heart defect. Congenital means present at birth.

How serious is a small hole in the heart?

The hole increases the amount of blood that flows through the lungs and over time, it may cause damage to the blood vessels in the lungs. Damage to the blood vessels in the lungs may cause problems in adulthood, such as high blood pressure in the lungs and heart failure.