What are the symptoms of Susac syndrome?

What are the symptoms of Susac syndrome?

What are the symptoms of Susac syndrome?

• Severe headache, often with vomiting.
• Confusion.
• Problems with thinking, such as short-term memory loss, slow thought processing and reduced ability to solve problems.
• Slurred speech.
• Walking difficulties.
• Changes in personality.

How do you get Susac syndrome?

Causes. Susac syndrome is an autoimmune endotheliopathy, a disorder in which the body’s immune system mistakenly attacks the inside lining (endothelium) of the walls of the very tiny blood vessels that supply blood to the brain, retina, and inner ear. The exact, underlying reason why this occurs is unknown.

What is the treatment for Susac syndrome?

Treatment requires immunosuppression. High-dose corticosteroid therapy is the mainstay, but additional therapies such as intravenous immunoglobulin, mycophenolate mofetil, and cyclophosphamide are often necessary. Rituximab is the newest therapy to consider.

What autoimmune disease causes Meniere’s disease?

An autoimmune disease, such as diabetes, lupus, or rheumatoid arthritis. Had a head injury, especially if it involved your ear. Had a viral infection of the inner ear.

What is Cogan syndrome?

Cogan’s syndrome is defined as a chronic inflammatory disease of unknown origin, an autoimmune disease, characterized by bilateral sensorineural hearing loss, vestibular symptoms, inflammatory ocular manifestations with variable risk of developing into a systemic disease.

How do you cure AIED?

The treatment most widely used for AIED is corticosteroids therapy. The initial dosage regimen is 60 mg or 1 mg/kg per day of prednisone or 6-methylprednisolone for a month. Shorter courses or lower doses have proved to be ineffective and increase the risk of relapse[24].

How many cases of Susac syndrome are there?

Susac syndrome (SuS) prevalence is still unknown. To date more than 500 cases have been reported worldwide. Young females (20-40 years) are more affected (female: male ratio 3.5:1). The age at onset ranges from 8 to 72 years (mean age: 32 years).

Is Meniere’s disease fatal?

Although it can be troublesome, Meniere’s disease is not contagious, and it isn’t fatal. Meniere’s disease is a chronic (ongoing) problem. People who have Meniere’s disease don’t have symptoms all the time. When symptoms occur, it’s called an “attack.” Attacks may happen often or just sometimes.

What body system is affected by Meniere’s disease?

Overview. Meniere’s disease is a disorder of the inner ear that can lead to dizzy spells (vertigo) and hearing loss. In most cases, Meniere’s disease affects only one ear. Meniere’s disease can occur at any age, but it usually starts between young and middle-aged adulthood.

What is livedo reticularis?

Livedo reticularis is thought to be due to spasms of the blood vessels or a problem of the blood flow near the skin surface. It makes the skin look mottled in sort of a net pattern with clear borders. The condition most often shows up on the legs. Sometimes livedo reticularis is simply the result of being chilled.

Can Raynaud’s cause dementia?

People with Sneddon syndrome may also have symptoms of Raynaud’s phenomenon, where blood flow to fingers and toes is restricted. Sneddon is also linked with an increased risk of high blood pressure, kidney problems, heart valve disease and dementia.